18-Lupen-3-one
Artikel-Nr:
(BOSSBS-15484R-CY7)
Lieferant:
Bioss
Hersteller-Artikelnummer::
BS-15484R-CY7
Lokale Artikelnummer::
BOSSBS-15484R-CY7
Beschreibung:
HIBCH is a 386 amino acid protein belonging to the enoyl-CoA hydratase/isomerase family. Localising to the mitochondria, HIBCH is highly expressed in liver and kidney, with lower levels found in heart, muscle and brain. HIBCH hydrolyses HIBYL-CoA, a saline catabolite, and _-hydroxypropionyl-CoA, an intermediate in the minor pathway involved in the metabolism of proprionate. Existing as two alternatively spliced isoforms, the gene encoding HIBCH maps to human chromosome 2q32.2. Defects to this gene result in HIBCH deficiency (HIBCHD), known alternatively as deficiency of _-hydroxyisobutyryl CoA deacylase or methacrylic aciduria. HIBCHD is characterised by the accumulation of methacrylyl-CoA, a highly reactive compound that undergoes addition reactions with free sulfhydryl groups. Phenotypic symptoms include early deterioration of neurological function, delayed motor skill development and hypotonia.
VE:
1 * 100 µl
Artikel-Nr:
(BOSSBS-15484R-CY5)
Lieferant:
Bioss
Hersteller-Artikelnummer::
BS-15484R-CY5
Lokale Artikelnummer::
BOSSBS-15484R-CY5
Beschreibung:
HIBCH is a 386 amino acid protein belonging to the enoyl-CoA hydratase/isomerase family. Localising to the mitochondria, HIBCH is highly expressed in liver and kidney, with lower levels found in heart, muscle and brain. HIBCH hydrolyses HIBYL-CoA, a saline catabolite, and _-hydroxypropionyl-CoA, an intermediate in the minor pathway involved in the metabolism of proprionate. Existing as two alternatively spliced isoforms, the gene encoding HIBCH maps to human chromosome 2q32.2. Defects to this gene result in HIBCH deficiency (HIBCHD), known alternatively as deficiency of _-hydroxyisobutyryl CoA deacylase or methacrylic aciduria. HIBCHD is characterised by the accumulation of methacrylyl-CoA, a highly reactive compound that undergoes addition reactions with free sulfhydryl groups. Phenotypic symptoms include early deterioration of neurological function, delayed motor skill development and hypotonia.
VE:
1 * 100 µl
Artikel-Nr:
(BOSSBS-15484R)
Lieferant:
Bioss
Hersteller-Artikelnummer::
BS-15484R
Lokale Artikelnummer::
BOSSBS-15484R
Beschreibung:
HIBCH is a 386 amino acid protein belonging to the enoyl-CoA hydratase/isomerase family. Localizing to the mitochondria, HIBCH is highly expressed in liver and kidney, with lower levels found in heart, muscle and brain. HIBCH hydrolyzes HIBYL-CoA, a saline catabolite, and β-hydroxypropionyl-CoA, an intermediate in the minor pathway involved in the metabolism of proprionate. Existing as two alternatively spliced isoforms, the gene encoding HIBCH maps to human chromosome 2q32.2. Defects to this gene result in HIBCH deficiency (HIBCHD), known alternatively as deficiency of β-hydroxyisobutyryl CoA deacylase or methacrylic aciduria. HIBCHD is characterized by the accumulation of methacrylyl-CoA, a highly reactive compound that undergoes addition reactions with free sulfhydryl groups. Phenotypic symptoms include early deterioration of neurological function, delayed motor skill development and hypotonia.
VE:
1 * 100 µl
Artikel-Nr:
(BOSSBS-15484R-A647)
Lieferant:
Bioss
Hersteller-Artikelnummer::
BS-15484R-A647
Lokale Artikelnummer::
BOSSBS-15484R-A647
Beschreibung:
HIBCH is a 386 amino acid protein belonging to the enoyl-CoA hydratase/isomerase family. Localising to the mitochondria, HIBCH is highly expressed in liver and kidney, with lower levels found in heart, muscle and brain. HIBCH hydrolyses HIBYL-CoA, a saline catabolite, and _-hydroxypropionyl-CoA, an intermediate in the minor pathway involved in the metabolism of proprionate. Existing as two alternatively spliced isoforms, the gene encoding HIBCH maps to human chromosome 2q32.2. Defects to this gene result in HIBCH deficiency (HIBCHD), known alternatively as deficiency of _-hydroxyisobutyryl CoA deacylase or methacrylic aciduria. HIBCHD is characterised by the accumulation of methacrylyl-CoA, a highly reactive compound that undergoes addition reactions with free sulfhydryl groups. Phenotypic symptoms include early deterioration of neurological function, delayed motor skill development and hypotonia.
VE:
1 * 100 µl
Artikel-Nr:
(BOSSBS-15484R-A488)
Lieferant:
Bioss
Hersteller-Artikelnummer::
BS-15484R-A488
Lokale Artikelnummer::
BOSSBS-15484R-A488
Beschreibung:
HIBCH is a 386 amino acid protein belonging to the enoyl-CoA hydratase/isomerase family. Localising to the mitochondria, HIBCH is highly expressed in liver and kidney, with lower levels found in heart, muscle and brain. HIBCH hydrolyses HIBYL-CoA, a saline catabolite, and _-hydroxypropionyl-CoA, an intermediate in the minor pathway involved in the metabolism of proprionate. Existing as two alternatively spliced isoforms, the gene encoding HIBCH maps to human chromosome 2q32.2. Defects to this gene result in HIBCH deficiency (HIBCHD), known alternatively as deficiency of _-hydroxyisobutyryl CoA deacylase or methacrylic aciduria. HIBCHD is characterised by the accumulation of methacrylyl-CoA, a highly reactive compound that undergoes addition reactions with free sulfhydryl groups. Phenotypic symptoms include early deterioration of neurological function, delayed motor skill development and hypotonia.
VE:
1 * 100 µl
Artikel-Nr:
(BOSSBS-15484R-A555)
Lieferant:
Bioss
Hersteller-Artikelnummer::
BS-15484R-A555
Lokale Artikelnummer::
BOSSBS-15484R-A555
Beschreibung:
HIBCH is a 386 amino acid protein belonging to the enoyl-CoA hydratase/isomerase family. Localising to the mitochondria, HIBCH is highly expressed in liver and kidney, with lower levels found in heart, muscle and brain. HIBCH hydrolyses HIBYL-CoA, a saline catabolite, and _-hydroxypropionyl-CoA, an intermediate in the minor pathway involved in the metabolism of proprionate. Existing as two alternatively spliced isoforms, the gene encoding HIBCH maps to human chromosome 2q32.2. Defects to this gene result in HIBCH deficiency (HIBCHD), known alternatively as deficiency of _-hydroxyisobutyryl CoA deacylase or methacrylic aciduria. HIBCHD is characterised by the accumulation of methacrylyl-CoA, a highly reactive compound that undergoes addition reactions with free sulfhydryl groups. Phenotypic symptoms include early deterioration of neurological function, delayed motor skill development and hypotonia.
VE:
1 * 100 µl
Artikel-Nr:
(BOSSBS-15484R-A680)
Lieferant:
Bioss
Hersteller-Artikelnummer::
BS-15484R-A680
Lokale Artikelnummer::
BOSSBS-15484R-A680
Beschreibung:
HIBCH is a 386 amino acid protein belonging to the enoyl-CoA hydratase/isomerase family. Localising to the mitochondria, HIBCH is highly expressed in liver and kidney, with lower levels found in heart, muscle and brain. HIBCH hydrolyses HIBYL-CoA, a saline catabolite, and _-hydroxypropionyl-CoA, an intermediate in the minor pathway involved in the metabolism of proprionate. Existing as two alternatively spliced isoforms, the gene encoding HIBCH maps to human chromosome 2q32.2. Defects to this gene result in HIBCH deficiency (HIBCHD), known alternatively as deficiency of _-hydroxyisobutyryl CoA deacylase or methacrylic aciduria. HIBCHD is characterised by the accumulation of methacrylyl-CoA, a highly reactive compound that undergoes addition reactions with free sulfhydryl groups. Phenotypic symptoms include early deterioration of neurological function, delayed motor skill development and hypotonia.
VE:
1 * 100 µl
Artikel-Nr:
(SIAL779342-100ML)
Lieferant:
Sigma-Aldrich
Hersteller-Artikelnummer::
779342-100ML
Lokale Artikelnummer::
SIAL779342-100ML
Beschreibung:
(±)-2,3-Epoxypropylmethacrylat
VE:
1 * 100 mL
Lieferant:
Sigma-Aldrich
Beschreibung:
(±)-2,3-Epoxypropylmethacrylat, Sigma-Aldrich®
Artikel-Nr:
(SIAL367664-5G)
Lieferant:
Sigma-Aldrich
Hersteller-Artikelnummer::
367664-5G
Lokale Artikelnummer::
SIAL367664-5G
Beschreibung:
1,1,1,3,3,3-Hexafluorisopropylmethacrylat, Sigma-Aldrich®
VE:
1 * 5 g
Artikel-Nr:
(BOSSBS-15484R-HRP)
Lieferant:
Bioss
Hersteller-Artikelnummer::
BS-15484R-HRP
Lokale Artikelnummer::
BOSSBS-15484R-HRP
Beschreibung:
HIBCH is a 386 amino acid protein belonging to the enoyl-CoA hydratase/isomerase family. Localising to the mitochondria, HIBCH is highly expressed in liver and kidney, with lower levels found in heart, muscle and brain. HIBCH hydrolyses HIBYL-CoA, a saline catabolite, and _-hydroxypropionyl-CoA, an intermediate in the minor pathway involved in the metabolism of proprionate. Existing as two alternatively spliced isoforms, the gene encoding HIBCH maps to human chromosome 2q32.2. Defects to this gene result in HIBCH deficiency (HIBCHD), known alternatively as deficiency of _-hydroxyisobutyryl CoA deacylase or methacrylic aciduria. HIBCHD is characterised by the accumulation of methacrylyl-CoA, a highly reactive compound that undergoes addition reactions with free sulfhydryl groups. Phenotypic symptoms include early deterioration of neurological function, delayed motor skill development and hypotonia.
VE:
1 * 100 µl
Lieferant:
FLUOROCHEM
Beschreibung:
2,2,2-Trifluorethylmethacrylat
Artikel-Nr:
(BOSSBS-15484R-CY3)
Lieferant:
Bioss
Hersteller-Artikelnummer::
BS-15484R-CY3
Lokale Artikelnummer::
BOSSBS-15484R-CY3
Beschreibung:
HIBCH is a 386 amino acid protein belonging to the enoyl-CoA hydratase/isomerase family. Localising to the mitochondria, HIBCH is highly expressed in liver and kidney, with lower levels found in heart, muscle and brain. HIBCH hydrolyses HIBYL-CoA, a saline catabolite, and _-hydroxypropionyl-CoA, an intermediate in the minor pathway involved in the metabolism of proprionate. Existing as two alternatively spliced isoforms, the gene encoding HIBCH maps to human chromosome 2q32.2. Defects to this gene result in HIBCH deficiency (HIBCHD), known alternatively as deficiency of _-hydroxyisobutyryl CoA deacylase or methacrylic aciduria. HIBCHD is characterised by the accumulation of methacrylyl-CoA, a highly reactive compound that undergoes addition reactions with free sulfhydryl groups. Phenotypic symptoms include early deterioration of neurological function, delayed motor skill development and hypotonia.
VE:
1 * 100 µl
Artikel-Nr:
(BOSSBS-15484R-A750)
Lieferant:
Bioss
Hersteller-Artikelnummer::
BS-15484R-A750
Lokale Artikelnummer::
BOSSBS-15484R-A750
Beschreibung:
HIBCH is a 386 amino acid protein belonging to the enoyl-CoA hydratase/isomerase family. Localising to the mitochondria, HIBCH is highly expressed in liver and kidney, with lower levels found in heart, muscle and brain. HIBCH hydrolyses HIBYL-CoA, a saline catabolite, and _-hydroxypropionyl-CoA, an intermediate in the minor pathway involved in the metabolism of proprionate. Existing as two alternatively spliced isoforms, the gene encoding HIBCH maps to human chromosome 2q32.2. Defects to this gene result in HIBCH deficiency (HIBCHD), known alternatively as deficiency of _-hydroxyisobutyryl CoA deacylase or methacrylic aciduria. HIBCHD is characterised by the accumulation of methacrylyl-CoA, a highly reactive compound that undergoes addition reactions with free sulfhydryl groups. Phenotypic symptoms include early deterioration of neurological function, delayed motor skill development and hypotonia.
VE:
1 * 100 µl
Artikel-Nr:
(REST30299)
Lieferant:
Restek
Hersteller-Artikelnummer::
30299
Lokale Artikelnummer::
REST30299
Beschreibung:
Organic Standard, Methyl methacrylate, 1 ml/ampoule
VE:
1 * 1 ST
Lieferant:
Sigma-Aldrich
Beschreibung:
Octadecylmethacrylat, Sigma-Aldrich®
Preis auf Anfrage
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